Porphobilinogen PBG

The test is used to diagnose porphyria. Porphyria is an inherited or acquired deficiency of the enzum of the heme synthesis pathway. In acute porphyria there is acute abdominal pain, bloating and nausea.


Significant amounts of porphobilinogen in the urine cause it to change its color to the color of port wine, after a few minutes of exposure to light.